Anesthetic considerations in Morquio syndrome: A case report

  • Thorat Pravin Shivajirao Department of Anesthesiology and Critical Care Rural Medical College, Pravara Institute of Medical Sciences, Loni 413736 (India)
  • Nageshkumar P Wasmatkar Department of Anesthesiology and Critical Care Rural Medical College, Pravara Institute of Medical Sciences, Loni 413736 (India)
  • Pratibha Govindrao Gore Department of Oral Pathology and Microbiology Rural Dental College, Pravara Institute of Medical Sciences, Loni 413736 (India)
  • J. N. Lakhe Department of Anesthesiology and Critical Care Rural Medical College, Pravara Institute of Medical Sciences, Loni 413736 (India)
  • Shidhaye Ramchandra Vinayak Department of Anesthesiology and Critical Care Rural Medical College, Pravara Institute of Medical Sciences, Loni 413736 (India)
Keywords: Morquio syndrome, Inhalation induction, Difficult intubation

Abstract

Anesthetic challenges in Morquio syndrome include the respiratory problems due to restrictive defect in the
thoracic cage, upper airway obstruction during head flexion, atlantoaxial instability and compression of the
cervical spinal cord due to hypoplasia of the dens, complicating intubation. After pre-anesthetic check up and
informed written consent, the patient was premedicated with glycopyrrolate 0.08 mg and fentanyl 10 mcg.
Induction was done with inhalational anesthetic agent sevoflurane along with Oxygen (O2) and Nitrous oxide
(N2O) maintaining the spontaneous respiration. Intubation was done with Flexo metallic tube (FMT) no. 24
through right nostril avoiding forceful movements at atlantoaxial joint and cervical spine. Maintenance and
recovery was uneventful. Paramount in the anaesthetic care of such patients is a thorough preoperative evaluation
of airway in addition to cardiac, respiratory, neurological function. Inhalational induction technique may be
useful in difficult intubation.

Published
01-30-2019
How to Cite
Shivajirao, T. P., Wasmatkar, N. P., Gore, P. G., Lakhe, J. N., & Vinayak, S. R. (2019). Anesthetic considerations in Morquio syndrome: A case report. Anaesthesia, Pain & Intensive Care, 75-78. Retrieved from https://apicareonline.com/index.php/APIC/article/view/468
Issue
Vol.17 No.1(2013): January-April
Section
Case Reports